Nephropathic Cystinosis in Adults: Natural History and Effects of Oral Cysteamine Therapy

Figure 2. One hundred adults with cystinosis received cysteamine for a certain period of time and then did not receive cysteamine for a defined period of time, and each patient had or did not have a specific complication at the time of admission. Duration of cysteamine therapy was grouped in 10-year increments. The frequencies of diabetes, myopathy, pulmonary dysfunction, and death increased with time off cysteamine therapy and decreased with time on cysteamine therapy.
Figure 2. One hundred adults with cystinosis received cysteamine for a certain period of time and then did not receive cysteamine for a defined period of time, and each patient had or did not have a specific complication at the time of admission. Duration of cysteamine therapy was grouped in 10-year increments. The frequencies of diabetes, myopathy, pulmonary dysfunction, and death increased with time off cysteamine therapy and decreased with time on cysteamine therapy. Frequency of cystinosis complications, by duration of oral cysteamine therapy.

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  1. Ann Intern Med August 21, 2007 vol. 147 no. 4 242-250
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